K. Verhelst, R. van Laere, De Eerste Wereldoorlog in Limburg. Verslagen, I, II
نویسندگان
چکیده
منابع مشابه
Brown-Vialetto-Van Laere syndrome
The Brown-Vialetto-Van Laere syndrome (BVVL) is a rare neurological disorder characterized by progressive pontobulbar palsy associated with sensorineural deafness. Fifty-eight cases have been reported in just over 100 years. The female to male ratio is approximately 3:1. The age of onset of the initial symptom varies from infancy to the third decade. The syndrome most frequently presents with s...
متن کاملمروری برسندرم Brown-Vialetto-Van Laere و تشخیصهای افتراقی آن
زمینه: سندرم Brown-Vialetto-Van Laere یکی از بیماریهای تحلیل برنده نورولوژیک است که جزء اختلالات نورون حرکتی طبقهبندی میشود. این سندرم بهلحاظ اپیدمیولوژیک نادر بوده اما در مناطق مختلف دنیا گزارش شده است. تظاهر بیماری اغلب بهصورت کاهش شنوایی دوطرفه و فلج پیشرونده پونتوبولبر است. درگیری بخش موتور اعصاب کرانیال تحتانی نیز دیده میشود. تشخیص بر اساس یافتههای بالینی و الکتروفیزیولوژی و رد نمود...
متن کاملPonto-bulbar palsy with deafness (Vialetto-Van Laere syndrome).
The syndrome described by Brown(l) Vialetto(2) and Van Laere(3) is a rare, often familial, characterized by bilateral nerve deafness followed or accompanied by involvement of various motor cranial nerves, e.g., 7th and 9th to 12th, rarely 3rd, 5th and 6th. On rare occasions, there may also be involvement of spinal motor nerves and less commonly of upper motor neurons. The onset of the disease i...
متن کاملBrown-Vialetto-van Laere syndrome; the first Turkish case.
We describe a 14-year-old female patient with progressive ponto-bulbar palsy and deafness. The first symptom was present at the age of 9 as a difficulty in walking and then she was stable with mild clumsy walking till 14 year-old. It was noticed that she had rapidly progression gait disorder, hearing loss, difficulty in swallowing and speaking in a period of 2.5 months. Clinically, there were b...
متن کاملBulbo-pontine paralysis with deafness: the Vialetto-Van Laere syndrome.
A Caucasian girl developed slowly progressive sensory neural deafness and bulbar and spinal muscle weakness typical of the Vialetto-Van Laere syndrome. As the condition progressed the major disabilities became dysphagia, respiratory muscle weakness and postural hypotension. Treatment with gastrostomy feedings, oxygen and fludrocortisone acetate produced worthwhile functional improvement.
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ژورنال
عنوان ژورنال: BMGN - Low Countries Historical Review
سال: 1999
ISSN: 2211-2898,0165-0505
DOI: 10.18352/bmgn-lchr.5060